[Congenital optic nerve pit associated with foveolar retinoschisis].

Objective/methods: The case of a 36 year old woman who complains of suffering a progressive decrease in visual acuity over a several year period is presented. Her corrected visual acuity was: 1.0 right eye and 0.7 in the left eye. The slit-lamp biomicroscopic examination showed an optic nerve pit in the left eye associated with a transparent schisislike separation of the inner macular retina with a stellate pattern, because of fine folds of the internal limiting membrane. The fluorescein angiography (F.A.) and visual field (V.F.) were normal.
Results/conclusion: Congenital optic pits are asymptomatic, unless a serous macular detachment complicates this entity. The characteristic image is an elevation of the neurosensorial retina, a transmission defect in the F.A. and a central scotoma. On the contrary, our patient had a foveolar schisis pattern with normal F.A. and V.F. This macula pattern is rarely associated with a congenital pit.