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Pulmonary arteriovenous fistula in the newborn: a case report of Rendu-Osler-Weber syndrome and a review of the literature.
- Source :
-
The Turkish journal of pediatrics [Turk J Pediatr] 2001 Oct-Dec; Vol. 43 (4), pp. 332-7. - Publication Year :
- 2001
-
Abstract
- In most instances, congenital arteriovenous fistula is only one manifestation of a more widespread abnormality; 60% of patients also have hereditary hemorrhagic telangiectasis (Rendu-Osler-Weber syndrome). Among those with congenital pulmonary arteriovenous fistula, the diagnosis is made during infancy in only 15% of patients. We present a case of pulmonary arteriovenous fistula in a newborn and review the literature. This rare condition of newborns can be treated with different surgical procedures. Only 17 cases of newborn pulmonary arteriovenous fistula/have been reported, and only two of those had associated Rendu-Osler-Weber syndrome. The results of surgical procedures were good in most of these cases. We treated our case with lobectomy successfully.
- Subjects :
- Arteriovenous Fistula genetics
Arteriovenous Fistula surgery
Female
Humans
Infant, Newborn
Pedigree
Telangiectasia, Hereditary Hemorrhagic genetics
Treatment Outcome
Arteriovenous Fistula diagnosis
Cyanosis congenital
Pulmonary Artery abnormalities
Telangiectasia, Hereditary Hemorrhagic diagnosis
Subjects
Details
- Language :
- English
- ISSN :
- 0041-4301
- Volume :
- 43
- Issue :
- 4
- Database :
- MEDLINE
- Journal :
- The Turkish journal of pediatrics
- Publication Type :
- Academic Journal
- Accession number :
- 11765165