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Pulmonary arteriovenous fistula in the newborn: a case report of Rendu-Osler-Weber syndrome and a review of the literature.

Authors :
Olguntürk R
Oğuz D
Tunaoğlu S
Ikizler C
Sezgin A
Kula S
Source :
The Turkish journal of pediatrics [Turk J Pediatr] 2001 Oct-Dec; Vol. 43 (4), pp. 332-7.
Publication Year :
2001

Abstract

In most instances, congenital arteriovenous fistula is only one manifestation of a more widespread abnormality; 60% of patients also have hereditary hemorrhagic telangiectasis (Rendu-Osler-Weber syndrome). Among those with congenital pulmonary arteriovenous fistula, the diagnosis is made during infancy in only 15% of patients. We present a case of pulmonary arteriovenous fistula in a newborn and review the literature. This rare condition of newborns can be treated with different surgical procedures. Only 17 cases of newborn pulmonary arteriovenous fistula/have been reported, and only two of those had associated Rendu-Osler-Weber syndrome. The results of surgical procedures were good in most of these cases. We treated our case with lobectomy successfully.

Details

Language :
English
ISSN :
0041-4301
Volume :
43
Issue :
4
Database :
MEDLINE
Journal :
The Turkish journal of pediatrics
Publication Type :
Academic Journal
Accession number :
11765165