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Thoracic lymphangiomatosis in a child.
- Source :
-
Journal of pediatric hematology/oncology [J Pediatr Hematol Oncol] 2004 Feb; Vol. 26 (2), pp. 136-41. - Publication Year :
- 2004
-
Abstract
- An 8-year-old boy who presented with a mediastinal mass, pulmonary infiltrates, and disseminated intravascular coagulation was diagnosed with lymphangiomatosis. Despite medical management, he developed multiple organ failure and died. The authors discuss the diagnostic findings, medical management, and pathology and review 52 additional cases of thoracic lymphangiomatosis from the literature. Patients presented with chylothorax (49%), a mass (47%), pulmonary infiltrates (45%), bone lesions (39%), splenic lesions (19%), cervical involvement (15%), disseminated intravascular coagulation (9%), and skin involvement (7%). Children (<16 years) had a worse prognosis than older patients (39% vs. 0% mortality). All patients who died had either parenchymal lung involvement or pleural effusion. Thoracic lymphangiomatosis should be included in the differential diagnosis of a mediastinal mass with pulmonary findings.
- Subjects :
- Child
Disseminated Intravascular Coagulation etiology
Fatal Outcome
Humans
Lung Neoplasms diagnostic imaging
Lung Neoplasms therapy
Lymphangioma diagnostic imaging
Lymphangioma therapy
Male
Mediastinal Neoplasms therapy
Pleural Effusion, Malignant etiology
Radiography
Disseminated Intravascular Coagulation therapy
Lung Neoplasms pathology
Lymphangioma pathology
Mediastinal Neoplasms pathology
Subjects
Details
- Language :
- English
- ISSN :
- 1077-4114
- Volume :
- 26
- Issue :
- 2
- Database :
- MEDLINE
- Journal :
- Journal of pediatric hematology/oncology
- Publication Type :
- Academic Journal
- Accession number :
- 14767208
- Full Text :
- https://doi.org/10.1097/00043426-200402000-00018