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Transient monoparesis after blade plate removal in a Hutchinson-Gilford progeria syndrome patient: a case report.

Authors :
Yandow SM
Rimoin DL
Grace AM
Fillman RR
Raney EM
Source :
Journal of pediatric orthopedics. Part B [J Pediatr Orthop B] 2009 May; Vol. 18 (3), pp. 151-6.
Publication Year :
2009

Abstract

Treatment of patients with Hutchinson-Gilford progeria syndrome (HGPS) is based on the abnormalities of accelerated aging that affect the healing processes, combined with a fragile cardiovascular status. A classic HGPS case, of Korean ancestry, previously treated for severe coxa valga with bilateral varus osteotomies using blade plate fixation is presented. Complications over the blade plate area required removal of the hardware, after which the patient showed right-sided hypertonicity--determined to be a cerebrovascular accident. Subsequently, the patient returned almost completely to her presurgical neurologic status. Perioperative planning for HGPS patients should include risks that are typically considered in the planning for geriatric patient care.

Details

Language :
English
ISSN :
1473-5865
Volume :
18
Issue :
3
Database :
MEDLINE
Journal :
Journal of pediatric orthopedics. Part B
Publication Type :
Academic Journal
Accession number :
19373113
Full Text :
https://doi.org/10.1097/BPB.0b013e32832ab928