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Mondini deformity in a case of Turner syndrome. A radiological finding.
- Source :
-
Acta otorrinolaringologica espanola [Acta Otorrinolaringol Esp] 2012 Sep-Oct; Vol. 63 (5), pp. 393-5. Date of Electronic Publication: 2011 May 06. - Publication Year :
- 2012
-
Abstract
- Turner syndrome (TS) is the human being's most frequent sex chromosome abnormality. Progressive sensorineural hearing loss is documented in more than 50% of the women affected by this syndrome. Although Mondini defect is the cochlear congenital malformation most frequently identified in other polymalformative syndromes, it has rarely been reported in TS. We describe the case of a 32-year-old woman with TS who presented progressive sensorineural hearing loss. The computed tomography of the ears showed bilateral Mondini deformity.<br /> (Copyright © 2010 Elsevier España, S.L. All rights reserved.)
- Subjects :
- Adult
Audiometry, Pure-Tone
Cochlea diagnostic imaging
Disease Progression
Female
Hearing Aids
Hearing Loss, Bilateral diagnosis
Hearing Loss, Sensorineural diagnosis
Humans
Middle Ear Ventilation
Otitis Media complications
Otitis Media surgery
Recurrence
Semicircular Canals diagnostic imaging
Tomography, X-Ray Computed
Turner Syndrome complications
Turner Syndrome diagnostic imaging
Vestibule, Labyrinth diagnostic imaging
Cochlea abnormalities
Hearing Loss, Bilateral etiology
Hearing Loss, Sensorineural etiology
Semicircular Canals abnormalities
Turner Syndrome pathology
Vestibule, Labyrinth abnormalities
Subjects
Details
- Language :
- English; Spanish; Castilian
- ISSN :
- 1988-3013
- Volume :
- 63
- Issue :
- 5
- Database :
- MEDLINE
- Journal :
- Acta otorrinolaringologica espanola
- Publication Type :
- Academic Journal
- Accession number :
- 21529720
- Full Text :
- https://doi.org/10.1016/j.otorri.2011.03.001