Back to Search Start Over

D11Y SOD1 mutation and benign ALS: a consistent genotype-phenotype correlation.

Authors :
Del Grande A
Conte A
Lattante S
Luigetti M
Marangi G
Zollino M
Madia F
Bisogni G
Sabatelli M
Source :
Journal of the neurological sciences [J Neurol Sci] 2011 Oct 15; Vol. 309 (1-2), pp. 31-3. Date of Electronic Publication: 2011 Aug 11.
Publication Year :
2011

Abstract

We describe three sporadic ALS patients in which a D11Y SOD1 mutation was detected. All three patients disclosed a prolonged survival and a stereotypical distal limbs involvement in the initial stages of the disease. By this report we demonstrate that D11Y SOD1 mutation is associated with a peculiar phenotype and we confirm its probable pathogenetic role.<br /> (Copyright © 2011 Elsevier B.V. All rights reserved.)

Details

Language :
English
ISSN :
1878-5883
Volume :
309
Issue :
1-2
Database :
MEDLINE
Journal :
Journal of the neurological sciences
Publication Type :
Academic Journal
Accession number :
21839474
Full Text :
https://doi.org/10.1016/j.jns.2011.07.041