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Recurrent phosphaturic mesenchymal tumour of the temporal bone causing deafness and facial nerve palsy.
- Source :
-
The Journal of laryngology and otology [J Laryngol Otol] 2012 Jul; Vol. 126 (7), pp. 721-4. Date of Electronic Publication: 2012 May 29. - Publication Year :
- 2012
-
Abstract
- Objective: We describe the first reported case of a phosphaturic mesenchymal tumour, mixed connective tissue variant, invading the temporal bone.<br />Case Report: A female patient presented with increasing deafness. On examination there appeared to be a mass behind an intact tympanic membrane. Further radiological investigation showed a vascular mass occupying the middle ear, mastoid and internal auditory meatus. This was surgically resected and revealed to be a benign phosphaturic mesenchymal tumour, mixed connective tissue variant. The tumour recurred a year later, presenting as facial nerve palsy. A revision procedure was carried out; the tumour was excised with the sacrifice of a segment of the facial nerve, and a facial-hypoglossal nerve anastomosis was performed.<br />Conclusion: This case report highlights the occurrence of this benign but sometimes aggressive tumour, of which both clinicians and pathologists should be aware. Early recognition of the condition remains of utmost importance to minimise the debilitating consequences of long-term osteomalacia in affected patients, and to prevent extracranial and intracranial complications caused by the tumour.
- Subjects :
- Aged
Anastomosis, Surgical
Ear, Middle pathology
Ear, Middle surgery
Facial Nerve surgery
Facial Nerve Diseases diagnosis
Facial Nerve Diseases surgery
Female
Humans
Hypoglossal Nerve surgery
Hypophosphatemia etiology
Magnetic Resonance Imaging
Mesenchymoma complications
Mesenchymoma diagnosis
Mesenchymoma surgery
Neoplasms, Connective Tissue complications
Neoplasms, Connective Tissue surgery
Osteomalacia
Otologic Surgical Procedures methods
Paraneoplastic Syndromes
Reoperation
Skull Neoplasms complications
Skull Neoplasms diagnosis
Skull Neoplasms surgery
Temporal Bone pathology
Temporal Bone surgery
Deafness etiology
Facial Nerve Diseases etiology
Mesenchymoma pathology
Neoplasm Recurrence, Local
Neoplasms, Connective Tissue pathology
Skull Neoplasms pathology
Subjects
Details
- Language :
- English
- ISSN :
- 1748-5460
- Volume :
- 126
- Issue :
- 7
- Database :
- MEDLINE
- Journal :
- The Journal of laryngology and otology
- Publication Type :
- Academic Journal
- Accession number :
- 22642807
- Full Text :
- https://doi.org/10.1017/S0022215112000989