Intracranial aneurysm and recessive polycystic kidney disease: the third reported case.

Objective: To highlight the possible association of intracranial aneurysm with autosomal recessive polycystic kidney disease.
Design, Setting, and Patient: To our knowledge, this association has been reported only twice in the medical literature. We herein report the case of a 21-year-old man with autosomal recessive polycystic kidney disease, presenting with subarachnoid hemorrhage secondary to a ruptured intracranial aneurysm, at our institution.
Results: In the presence of only 3 cases in the medical literature, one might conclude they are a simple coincidence. However, should this association exist, such as with the dominant form, then the neurologic prognosis and even the life of young patients may be at stake.
Conclusions: Given the devastating consequences of intracranial bleeding in young patients, early neurologic screening may be warranted.