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A rare case of orbital haemangiopericytoma arising in childhood.
- Source :
-
Orbit (Amsterdam, Netherlands) [Orbit] 2013 Dec; Vol. 32 (6), pp. 384-6. Date of Electronic Publication: 2013 Jul 29. - Publication Year :
- 2013
-
Abstract
- Haemangiopericytoma (HPC) is a rare soft tissue tumour of fibroblastic origin and is part of the solitary fibrous tumour spectrum. The tumour is generally considered to be benign, but can behave clinically as if sarcomatous -- with relentless infiltrative local growth. HPC generally presents in adulthood (median age 45 years for orbital disease) and is equally frequent in both sexes. HPC can arise in any site in the body and presents as a slowly growing, painless mass. We report a case of a 20 year old African male seen at Kikuyu Eye Unit, Kenya, with a 12 year history of a gradually enlarging, painless orbital mass. The patient underwent skin-sparing orbital exenteration with complete tumour excision; histology confirmed diagnosis of HPC.
- Subjects :
- Actins metabolism
Antigens, CD34 metabolism
Biomarkers, Tumor metabolism
Complement C8 metabolism
Hemangiopericytoma metabolism
Hemangiopericytoma surgery
Humans
Male
Orbit Evisceration
Orbital Neoplasms metabolism
Orbital Neoplasms surgery
Young Adult
Hemangiopericytoma pathology
Orbital Neoplasms pathology
Subjects
Details
- Language :
- English
- ISSN :
- 1744-5108
- Volume :
- 32
- Issue :
- 6
- Database :
- MEDLINE
- Journal :
- Orbit (Amsterdam, Netherlands)
- Publication Type :
- Academic Journal
- Accession number :
- 23895036
- Full Text :
- https://doi.org/10.3109/01676830.2013.815226