ALCAPA and massive pulmonary atelectasis: how a stent in the airway can be life-saving.

Authors :: Serio P
Chiappa E
Fainardi V
Favilli S
Murzi B
Baggi R
Arcieri L
Leone R
Mirabile L
Source :: International journal of pediatric otorhinolaryngology [Int J Pediatr Otorhinolaryngol] 2014 Nov; Vol. 78 (11), pp. 2015-7. Date of Electronic Publication: 2014 Sep 06.
Publication Year :: 2014
Abstract: Anomalous left coronary artery from pulmonary artery (ALCAPA) is a rare congenital anomaly in which left coronary artery arises from the pulmonary artery resulting in progressive myocardial ischemia and dysfunction of the left ventricle. We report a case of ALCAPA with severe cardiac and respiratory failure and huge heart dilation compressing the left main bronchus and preventing from an effective ventilation. Emergency bronchial stenting allowed to improve left lung atelectasis, reduce pulmonary hypertension, resume anterograde left coronary artery perfusion and stabilize cardiovascular conditions to undertake a successful surgical correction.<br /> (Copyright © 2014 Elsevier Ireland Ltd. All rights reserved.)

Subjects :: Bronchi
Female
Heart Failure etiology
Humans
Hypertension, Pulmonary etiology
Hypertension, Pulmonary therapy
Infant
Pulmonary Atelectasis etiology
Respiratory Insufficiency etiology
Bland White Garland Syndrome complications
Heart Failure therapy
Pulmonary Atelectasis therapy
Respiratory Insufficiency therapy
Stents

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