Back to Search Start Over

[Diagnostic criteria and treatment progress of PHACE syndrome].

Authors :
Sun LL
Sun B
Ma YC
Lei HZ
Dong CX
Source :
Zhonghua kou qiang yi xue za zhi = Zhonghua kouqiang yixue zazhi = Chinese journal of stomatology [Zhonghua Kou Qiang Yi Xue Za Zhi] 2017 Nov 09; Vol. 52 (11), pp. 700-703.
Publication Year :
2017

Abstract

PHACE syndrome is a syndrome of multiple organ and multisystem abnormalities associated with infantile segmental hemangioma, characterized by abnormal posterior fossa development, infant hemangioma, aortic abnormalities, aortic coarctation and heart defects, eye anomalies and other symptoms. The incidence of the disease is low, but there exist life-threatening factors. Once clinically diagnosed, it should be highly valued and multidisciplinary consultation must be conducted. This article reviews the diagnostic criteria of PHACE syndrome and its associated facial segmental hemangioma, as well as the treatment and prognosis of brain abnormalities.

Details

Language :
Chinese
ISSN :
1002-0098
Volume :
52
Issue :
11
Database :
MEDLINE
Journal :
Zhonghua kou qiang yi xue za zhi = Zhonghua kouqiang yixue zazhi = Chinese journal of stomatology
Publication Type :
Academic Journal
Accession number :
29972952
Full Text :
https://doi.org/10.3760/cma.j.issn.1002-0098.2017.11.011