Back to Search
Start Over
Clathrin plaques and associated actin anchor intermediate filaments in skeletal muscle.
- Source :
-
Molecular biology of the cell [Mol Biol Cell] 2019 Mar 01; Vol. 30 (5), pp. 579-590. Date of Electronic Publication: 2019 Jan 02. - Publication Year :
- 2019
-
Abstract
- Clathrin plaques are stable features of the plasma membrane observed in several cell types. They are abundant in muscle, where they localize at costameres that link the contractile apparatus to the sarcolemma and connect the sarcolemma to the basal lamina. Here, we show that clathrin plaques and surrounding branched actin filaments form microdomains that anchor a three-dimensional desmin intermediate filament (IF) web. Depletion of clathrin plaque and branched actin components causes accumulation of desmin tangles in the cytoplasm. We show that dynamin 2, whose mutations cause centronuclear myopathy (CNM), regulates both clathrin plaques and surrounding branched actin filaments, while CNM-causing mutations lead to desmin disorganization in a CNM mouse model and patient biopsies. Our results suggest a novel paradigm in cell biology, wherein clathrin plaques act as platforms capable of recruiting branched cortical actin, which in turn anchors IFs, both essential for striated muscle formation and function.
- Subjects :
- Animals
Desmin metabolism
Dynamin II metabolism
Humans
Intermediate Filaments metabolism
Intermediate Filaments ultrastructure
Mice, Knockout
Muscle Fibers, Skeletal metabolism
Muscle Fibers, Skeletal ultrastructure
Mutation genetics
Myopathies, Structural, Congenital genetics
Wiskott-Aldrich Syndrome Protein metabolism
Actins metabolism
Clathrin metabolism
Muscle, Skeletal metabolism
Subjects
Details
- Language :
- English
- ISSN :
- 1939-4586
- Volume :
- 30
- Issue :
- 5
- Database :
- MEDLINE
- Journal :
- Molecular biology of the cell
- Publication Type :
- Academic Journal
- Accession number :
- 30601711
- Full Text :
- https://doi.org/10.1091/mbc.E18-11-0718