Back to Search
Start Over
Ultrasound findings in neonates with alveolar capillary dysplasia with misalignment of the pulmonary veins: report of two cases.
- Source :
-
The Journal of international medical research [J Int Med Res] 2022 Sep; Vol. 50 (9), pp. 3000605221126876. - Publication Year :
- 2022
-
Abstract
- Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACDMPV) is a rare congenital pulmonary disease that affects newborns. Most patients with ACDMPV are born at full term and are healthy. The main clinical manifestations are refractory pulmonary hypertension and pulmonary failure with gastrointestinal, urinary, or cardiac malformations. ACDMPV often progresses rapidly, but no conventional biological or imaging tests other than genetic testing are available for its diagnosis. Lung biopsy is currently the gold standard for diagnosis. We herein report two cases of ACDMPV confirmed by pathological examination and discuss their ultrasonographic findings.
- Subjects :
- Forkhead Transcription Factors genetics
Humans
Infant, Newborn
Pulmonary Alveoli abnormalities
Pulmonary Alveoli diagnostic imaging
Persistent Fetal Circulation Syndrome diagnostic imaging
Persistent Fetal Circulation Syndrome genetics
Pulmonary Veins abnormalities
Pulmonary Veins diagnostic imaging
Pulmonary Veins pathology
Subjects
Details
- Language :
- English
- ISSN :
- 1473-2300
- Volume :
- 50
- Issue :
- 9
- Database :
- MEDLINE
- Journal :
- The Journal of international medical research
- Publication Type :
- Academic Journal
- Accession number :
- 36173014
- Full Text :
- https://doi.org/10.1177/03000605221126876