Back to Search Start Over

Isolated embryonal rhabdomyosarcoma of the anterior petrous bone in a young child: Focusing on the intra-operative diagnosis and differentials.

Authors :
Panda I
Bethanbhatla MK
Gupta K
Salunke P
Source :
Clinical neuropathology [Clin Neuropathol] 2024 Mar-Apr; Vol. 43 (2), pp. 48-52.
Publication Year :
2024

Abstract

Objective: Rhabdomyosarcoma is a common soft tissue tumor, but isolated involvement of anterior portion of petrous bone is exceedingly rare. Here, we present a case of embryonal rhabdomyosarcoma involving the anterior petrous without involvement of the mastoid and middle ear.<br />Patient: A 6-year-old boy presented with a progressive right side lower motor neuron facial paresis for 1-month duration along with headache and recurrent vomiting episodes. Radiology showed a contrast-enhancing lesion involving the right petrous apex. He underwent craniotomy and excision of the lesion. Based on the frozen section, a diagnosis of rhabdomyosarcoma was rendered, and gross total resection could be achieved. Postoperative course was uneventful.<br />Conclusion: Isolated petrous bone involvement of embryonal rhabdomyosarcoma is a rare presentation. Intra-operative frozen section plays a key role in decision making regarding the extent of excision. Hence, a prompt and accurate diagnosis is essential in managing these cases.

Details

Language :
English
ISSN :
0722-5091
Volume :
43
Issue :
2
Database :
MEDLINE
Journal :
Clinical neuropathology
Publication Type :
Academic Journal
Accession number :
38085093
Full Text :
https://doi.org/10.5414/NP301586