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[Freeman-Sheldon syndrome: generalized muscular rigidity after anesthetic induction].

Authors :
Sobrado CG
Ribera M
Martí M
Erdocia J
Rodríguez R
Source :
Revista espanola de anestesiologia y reanimacion [Rev Esp Anestesiol Reanim] 1994 May-Jun; Vol. 41 (3), pp. 182-4.
Publication Year :
1994

Abstract

We describe a case of generalized muscle rigidity in a 2-year-old patient with Freeman-Sheldon syndrome undergoing surgery for eventration of the diaphragm after anesthetic induction with halothane and succinylcholine. Anesthetic induction was by mask with oxygen, nitrous oxide and halothane, with succinylcholine as a muscle relaxant. Approximately 10 minutes after start of induction, muscular rigidity appeared and developed rapidly, becoming severe and compromising ventilation. Tracheal intubation was attempted without success, owing to stiffness of the masseter muscles. Sodium dantrolene 2.5 mg/kg was administered and relaxation was achieved immediately for both masseter and peripheral muscles, such that the patient recovered spontaneous breathing. We conclude that there is risk of association between Freeman-Sheldon syndrome and malignant hyperthermia.

Details

Language :
Spanish; Castilian
ISSN :
0034-9356
Volume :
41
Issue :
3
Database :
MEDLINE
Journal :
Revista espanola de anestesiologia y reanimacion
Publication Type :
Academic Journal
Accession number :
8059048