Large-vessel occlusion in a patient with Emery-Dreifuss muscular dystrophy.

The article informs about heart problems in individuals with Emery- -Dreifuss muscular dystrophy are caused by a number of related complications. Topics include Cardiac complications manifest as arrhythmias, atrio-ventricular conduction blockages, congestive heart failure; and Cardiac involvement develops independently of changes in the neuromuscular system as patients should be examined in detail using electrocardiography (ECG), and invasive electrophysiological examination.