Kindler syndrome and role of dental surgeon: Providing quality oral health care -- A case report.

Introduction: Kindler syndrome is an autosomal recessive disorder with multisystem involvement such as cutaneous, oral, gastrointestinal, and urogenital manifestations. Rationale: Timely diagnosis and management of this syndrome are warranted. The dental surgeon has a prime role in diagnosing the same and halting the progression of gingivitis to periodontitis and referring the patient to appropriate specialists for effective and timely management of the same. Patient Concerns: In this case report, a 17-year-old patient had reported with the chief complaint of spontaneous bleeding from gums and swollen gums since birth, and blackish pigmentation of the skin. Diagnosis: On examination, the patient had poikiloderma, photosensitivity, gingival fragility, and skin atrophy suggesting a diagnosis of Kindler syndrome. Interventions: Oral prophylaxis was done for the patient on several sittings and the patient was on continuous follow-up for 2 years. Dermatology and urology opinions were sought and advice was followed. Outcomes: The patient had complete regression of spontaneous gingival bleeding and oral hygiene had also become satisfactory. Lesson: Prompt diagnosis of the disease with appropriate and early intervention by a dental surgeon could definitely stop the disease progression. [ABSTRACT FROM AUTHOR]