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Bilateral orbital involvement in Erdheim-Chester disease.
- Source :
- Orbit; Jun98, Vol. 17 Issue 2, p97-105, 9p
- Publication Year :
- 1998
-
Abstract
- Erdheim-Chester disease is an idiopathic condition characterized by a xanthogranulomatous process infiltrating the bones, lungs, heart, retroperitoneum and other tissues. This condition is often fatal. Ocular findings are rare. The authors report a case of bilateral xanthelasmas and bilateral massive orbital infiltration in a 61-year-old man with severe retroperitoneal fibrosis, renal and cardiovascular problems. The ophthalmic manifestations and differential diagnosis of this peculiar pathologic condition are discussed. [ABSTRACT FROM AUTHOR]
- Subjects :
- ORBITAL diseases
EYE diseases
Subjects
Details
- Language :
- English
- ISSN :
- 01676830
- Volume :
- 17
- Issue :
- 2
- Database :
- Complementary Index
- Journal :
- Orbit
- Publication Type :
- Academic Journal
- Accession number :
- 5306575
- Full Text :
- https://doi.org/10.1076/orbi.17.2.97.2758