Back to Search Start Over

Abnormal collagen metabolism in cultured cells in osteogenesis imperfecta.

Authors :
Penttinen, R P
Lichtenstein, J R
Martin, G R
McKusick, V A
Source :
Proceedings of the National Academy of Sciences of the United States of America; February 1975, Vol. 72 Issue: 2 p586-589, 4p
Publication Year :
1975

Abstract

Cells obtained from normal human skin synthesize predominantly type I collogen in culture. Cells obtained from the skin of an infant with a severe form of osteogenesis imperfecta were found to synthesize as much type III as type I collagen. Decreased synthesis of type I collagen could explain the tissue fragility observed in this case.

Details

Language :
English
ISSN :
00278424 and 10916490
Volume :
72
Issue :
2
Database :
Supplemental Index
Journal :
Proceedings of the National Academy of Sciences of the United States of America
Publication Type :
Periodical
Accession number :
ejs60428853
Full Text :
https://doi.org/10.1073/pnas.72.2.586