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A novel nonsense variant in TPM4caused dominant macrothrombocytopenia, mild bleeding tendency and disrupted cytoskeleton remodeling

Authors :
Marín‐Quílez, Ana
Vuelta, Elena
Díaz‐Ajenjo, Lorena
Fernández‐Infante, Cristina
García‐Tuñón, Ignacio
Benito, Rocío
Palma‐Barqueros, Verónica
Hernández‐Rivas, Jesús María
González‐Porras, José Ramón
Rivera, José
Bastida, José María
Source :
Journal of Thrombosis and Haemostasis; May 2022, Vol. 20 Issue: 5 p1248-1255, 8p
Publication Year :
2022

Abstract

Rare inherited thrombocytopenias are caused by alterations in genes involved in megakaryopoiesis, thrombopoiesis and/or platelet release. Diagnosis is challenging due to poor specificity of platelet laboratory assays, large numbers of culprit genes, and difficult assessment of the pathogenicity of novel variants.

Details

Language :
English
ISSN :
15387933 and 15387836
Volume :
20
Issue :
5
Database :
Supplemental Index
Journal :
Journal of Thrombosis and Haemostasis
Publication Type :
Periodical
Accession number :
ejs62064014
Full Text :
https://doi.org/10.1111/jth.15672