Skip to search
Skip to main content
Back to Search
Start Over
Childhood Langerhans cell histiocytosis hematological involvement: severity associated with BRAFV600Eloads
Authors :
Thalhammer, Julian Jeziorski, Eric Marec-Bérard, Perrine Barkaoui, Mohamed Aziz Pagnier, Anne Rohrlich, Pierre-Simon Chevallier, Aurore Carausu, Liana Aladjidi, Nathalie Rigaud, Charlotte Leruste, Amaury Azarnoush, Saba Lauvray, Thomas Le Louet, Solenne Gandemer, Virginie Treguier, Pauline Mansuy, Ludovic Pasquet, Marlene Olivier, Laura Rome, Angélique Saultier, Paul Isfan, Fiorentina Renard, Cécile Li Thiao Te, Valerie Salmon, Alexandra Blanc, Laurence Abou Chahla, Wadih Lambilliotte, Anne Stephan, Jean-Louis Geissmann, Frederic Lejeune, Julien Mallebranche, Coralie Reguerre, Yves Grain, Audrey Thomas, Caroline Hélias-Rodzewicz, Zofia Moshous, Despina Fenneteau, Odile Coulomb-L’Hermine, Aurore Lapillonne, Hélène de Saint-Basile, Geneviève Emile, Jean-François Héritier, Sébastien Donadieu, Jean Devoldere, Catherine Gourmel, Antoine Lutun, Anne Leglise, Sophie Pellier, Isabelle Proust, Stéphanie Cheikh, Nathalie Klein, Sébastien Simon, Pauline Verite, Cécile Miaz, Leila Bodet, Damien Deparis, Marianna Gaudichon, Jérémie Dore, Eric Kanold, Justyna Briandet, Claire Desplantes, Claire Neuman, Florent Adjaoud, Dalila Armari-Alla, Corinne Plantaz, Dominique Perret, Cécile Bruno, Bénedicte Nelken, Brigitte Piguet, Christophe Bertrand, Yves Garnier, Nathalie Kebaili, Kamila Ouachee, Marie Coze, Carole Curtillet, Catherine Gentet, Jean-Claude Michel, Gérard Galambrun, Claire Chastagner, Pascal Boutroux, Hélène Landman-Parker, Judith Bodak, Nathalie Leverger, Guy Petit, Arnaud Simonin, Mathieu Tabone, Marie-Dominique Bader-Meunier, Brigitte Blanche, Stéphane Castelle, Martin Neven, Bénédicte Bodemer, Christine Perrin, Olivia Boccara Aerts, Isabelle Orbach, Daniel Bourdeaut, Franck Brugieres, Laurence Dufour, Christelle Minard, Véronique Valteau-Couanet, Dominique Blanc, Laurence Millot, Frédéric Guimard, Grégory Pluchart, Claire Bonneau, Jacinthe Chappe, Céline Taque, Sophie Pertuisel, Sophie Gandemer, Virginie Probert, Jamie Puiseux, Chloé Buchbinder, Nimrod Dumesnil, Cécile Filhon, Bruno Marie-Cardine, Aude Schneider, Pascale Berger, Claire Thouvenin-Doulet, Sandrine Entz-Werle, Natacha Paillard, Catherine Spiegel, Alexandra Plat, Geneviève Blouin, Pascale Jourdain, Anne Yvert-Guillebert, Marion Jehanne, Mathilde Benadiba, Joy Soler, Christine Poiree, Maryline Haouy, Stéphanie Sirvent, Nicolas Saumet, Laure
Source :
Blood; March 2025, Vol. 145 Issue: 10 p1061-1073, 13p
Publication Year :
2025
Abstract
•LCH-HI is life threatening, defined as hemoglobin ≤7 g/dL and/or platelets ≤20 × 109/L.•LCH-HI severity, associated with BRAFV600Evariant and macrophage activation, may require early MAPK inhibitors.
Details
Language :
English
ISSN :
00064971 and 15280020
Volume :
145
Issue :
10
Database :
Supplemental Index
Journal :
Blood
Publication Type :
Periodical
Accession number :
ejs67904470
Full Text :
https://doi.org/10.1182/blood.2024025625