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Long-term Outcomes after Truncus Arteriosus Repair: A Single-center Experience for More than 40 Years
- Source :
- Congenital Heart Disease. 11:672-677
- Publication Year :
- 2016
- Publisher :
- Computers, Materials and Continua (Tech Science Press), 2016.
-
Abstract
- Objectives This study aimed to analyze long-term survival and functional outcomes after truncus arteriosus repair in a single institution with more than 40 years of follow-up. Methods Medical records were analyzed retrospectively in 52 patients who underwent the Rastelli procedure for truncus arteriosus repair between 1974 and 2002. Thirty-five patients survived the initial repair. The median age at the initial operation was 2.8 months (range, 0.1–123 months) and the body weight was 3.9 kg (range, 1.6 to 15.0 kg). Results The median age at follow-up was 23.6 years (range, 12.4 to 44.5 years). The median follow-up duration was 23.4 years (range, 12.3 to 40.7 years). The actuarial survival rate was 97% at 10 years and 93% at both 20 years and 40 years after the initial operation. At follow-up, most patients were in New York Heart Association (NYHA) functional classes I (73%) and II (24%). Thirty-six percent of patients had full-time jobs, 40% were students, and 21% were unemployed. Most patients (97%) had undergone conduit reoperations. Freedom from reoperation for right ventricular (RV) outflow and pulmonary artery (PA) stenosis was 59% at 5 years, 28% at 10 years, and 3% at 20 years after the initial operation. Freedom from catheter interventions for RV outflow and PA stenosis was 59% at 5 years, 47% at 10 years, and 38% at 20 years after the initial operation. Freedom from truncal valve replacement was 88% at 5 years, 85% at 10 years, and 70% at 20 years after the initial operation. Conclusions In this single-center retrospective study, with long-term follow-up after repair of truncus arteriosus, long-term survival and functional outcomes were acceptable, despite the requirement for reoperation and multiple catheter interventions for RV outflow and PA stenosis in almost all patients, and the frequent requirement for late truncal valve operations.
- Subjects :
- medicine.medical_specialty
medicine.medical_treatment
Persistent truncus arteriosus
Ventricular Outflow Obstruction
030204 cardiovascular system & hematology
Single Center
03 medical and health sciences
0302 clinical medicine
Internal medicine
medicine.artery
medicine
Radiology, Nuclear Medicine and imaging
Cardiac catheterization
business.industry
General Medicine
Rastelli procedure
medicine.disease
Surgery
Catheter
Stenosis
030228 respiratory system
Pediatrics, Perinatology and Child Health
Pulmonary artery
cardiovascular system
Cardiology
Cardiology and Cardiovascular Medicine
business
Subjects
Details
- ISSN :
- 1747079X
- Volume :
- 11
- Database :
- OpenAIRE
- Journal :
- Congenital Heart Disease
- Accession number :
- edsair.doi...........2c58b25b9379b64fa113611d4293fc78