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Congenitally Corrected Transposition of the Great Arteries and Situs Inversus in an Octogenarian With Systemic Right Ventricular Failure
- Source :
- International Heart Journal. 58:151-154
- Publication Year :
- 2017
- Publisher :
- International Heart Journal (Japanese Heart Journal), 2017.
-
Abstract
- Systemic right ventricular (RV) failure in patients with congenitally corrected transposition of the great arteries (ccTGA), a major cause of mortality in the long-term follow-up, is usually induced by concomitant severe morphologically tricuspid regurgitation (TR) with/without Ebstein's anomaly or progressive conduction tissue disturbances. However, whether or not myocardial fibrosis is a common cause of systemic RV failure in patients with ccTGA remains unclear. Here, we describe an 82-year-old man who had been diagnosed previously as having uncomplicated ccTGA and situs inversus and recently developed systemic RV failure, which was neither associated with severe TR nor advanced conduction tissue abnormalities. Cardiovascular magnetic resonance (CMR) with delayed-enhancement imaging clearly detected extensive myocardial scars (presumably fibrosis) in the RV wall as well as prominent dilatation, hypertrophy, and systolic dysfunction of the systemic RV. These findings suggest that myocardial fibrosis can cause systemic RV failure in elderly patients with uncomplicated ccTGA despite the absence of severe TR or advanced conduction tissue abnormalities and that CMR may be a useful examination to accurately detect systemic RV failure associated with myocardial fibrosis and to subsequently clarify the prognosis in these patients.
- Subjects :
- medicine.medical_specialty
medicine.diagnostic_test
business.industry
Scars
Magnetic resonance imaging
General Medicine
Regurgitation (circulation)
030204 cardiovascular system & hematology
medicine.disease
Surgery
Muscle hypertrophy
03 medical and health sciences
Situs inversus
0302 clinical medicine
Fibrosis
Great arteries
Internal medicine
Cardiology
Medicine
Myocardial fibrosis
medicine.symptom
Cardiology and Cardiovascular Medicine
business
030217 neurology & neurosurgery
Subjects
Details
- ISSN :
- 13493299 and 13492365
- Volume :
- 58
- Database :
- OpenAIRE
- Journal :
- International Heart Journal
- Accession number :
- edsair.doi...........d4de3ab7feae488cc919b104d67f7bd2