Transmastoid approach for surgical repair of superior canal dehiscence syndrome

Patients with superior canal dehiscence syndrome may present with a myriad of auditory and/or vestibular complaints. Treatment of superior canal dehiscence syndrome depends on severity of symptoms and impact on quality of life. Surgery is recommended for patients with debilitating auditory and/or vestibular symptoms. The goal of surgery is to create a durable and watertight seal of the bony superior semicircular canal defect, thereby eliminating the “third window”. Repair involves either resurfacing and/or plugging of the dehiscent superior canal to eliminate the third window and reduce symptoms. Surgical options include middle fossa craniotomy or transmastoid (TM) approach. The main advantages of a TM approach includes (1) avoidance of a craniotomy, (2) lower risk of CSF leak, and (3) no brain retraction. The TM approach is ideal for superior petrosal sinus superior canal dehiscence cases as the defect is found medial along the skull base and can be isolated indirectly without direct manipulation of the brain and sinus. This chapter discusses the surgical technique of TM approach.