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Degos disease: a case report and review of the literature
- Source :
- Journal of Medical Case Reports, Vol 14, Iss 1, Pp 1-4 (2020), Journal of Medical Case Reports
- Publication Year :
- 2020
- Publisher :
- BMC, 2020.
-
Abstract
- Background Degos disease is a very rare syndrome with multisystem vasculopathy of unknown cause. It can affect the skin, gastrointestinal tract, and central nervous system. However, other organs such as the kidney, lungs, pleura, and liver can also be involved. Case presentation A 35-year-old Hindu woman presented to our dermatology outpatient department with complaints of depigmented painful lesions. A skin punch biopsy taken from the porcelain white atrophic papules which revealed features of Degos disease. Conclusion The diagnosis of Degos disease is usually based on the presence of the pathognomonic skin lesions and a tissue biopsy demonstrating a wedge-shaped area of necrosis with thrombotic occlusion of the small arterioles. No specific treatment is currently available for this disease.
- Subjects :
- Adult
medicine.medical_specialty
Biopsy
Skin punch biopsy
Degos disease
lcsh:Medicine
Case Report
Vasculopathy
Disease
Skin Diseases
030207 dermatology & venereal diseases
03 medical and health sciences
Necrosis
0302 clinical medicine
Pathognomonic
Skin biopsy
Medicine
Outpatient clinic
Humans
Skin
Gastrointestinal tract
medicine.diagnostic_test
business.industry
lcsh:R
General Medicine
medicine.disease
Dermatology
Malignant Atrophic Papulosis
030211 gastroenterology & hepatology
Female
Malignant atrophic papulosis
business
Subjects
Details
- Language :
- English
- ISSN :
- 17521947
- Volume :
- 14
- Issue :
- 1
- Database :
- OpenAIRE
- Journal :
- Journal of Medical Case Reports
- Accession number :
- edsair.doi.dedup.....1ebf72d6739d298dd0a6a5651296ac4b