Sorry, I don't understand your search. ×
Back to Search Start Over

Case report of the broad spectrum of late complications in an adult patient with univentricular physiology palliated by the Fontan circulation

Case report of the broad spectrum of late complications in an adult patient with univentricular physiology palliated by the Fontan circulation

Authors :
Marieke Nederend
Anastasia D Egorova
Hubert W Vliegen
Arno A W Roest
Bastian N Ruijter
Tijmen Korteweg
Maarten K Ninaber
Katja Zeppenfeld
Mark G Hazekamp
Philippine Kiès
Monique R M Jongbloed
Source :
EUROPEAN HEART JOURNAL-CASE REPORTS, 6(2). OXFORD UNIV PRESS
Publication Year :
2022

Abstract

Background At the most severe end of the spectrum of congenital heart disease are patients with an univentricular physiology. They comprise a heterogeneous group of congenital heart malformations that have the common characteristic that the cardiac morphology is not equipped for sustaining a biventricular circulation. Case summary Here, we present a case of an adult patient after Fontan palliation, illustrative of the complex clinical course and the broad spectrum of complications that can be encountered during follow-up, highlighting the need for a multidisciplinary approach in the clinical care for these patients. Discussion During the surgical Fontan procedure, the inferior vena cava is connected to the pulmonary circulation, after prior connection of the superior vena cava to the pulmonary arterial circulation. The resulting cavopulmonary connection, thus lacking a subpulmonic ventricle, provides non-pulsatile passive flow of oxygen-poor blood from the systemic venous circulation into the lungs, and the functional monoventricle pumps the oxygen-rich pulmonary venous return blood into the aorta. With an operative mortality of Conclusion For optimal treatment, the evaluation in a multidisciplinary team is mandatory, using the specific expertise of the team members to timely detect and address late complications and to support quality of life.

Details

Language :
English
Database :
OpenAIRE
Journal :
EUROPEAN HEART JOURNAL-CASE REPORTS, 6(2). OXFORD UNIV PRESS
Accession number :
edsair.doi.dedup.....2173fbf7e3097a304aa469b48d882d66