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Wilson Disease in Children; Chelation Therapy or Liver Transplantation? A 10-Year Experience from Pakistan
- Source :
- Annals of Transplantation
- Publication Year :
- 2021
- Publisher :
- International Scientific Literature, Inc., 2021.
-
Abstract
- BACKGROUND Wilson disease (WD) is a rare genetic disorder with vast clinical presentations and a higher incidence in areas where consanguinity is common. Most patients can be treated with oral chelation, but some require advanced surgical intervention, like liver transplantation (LT). This study aims to review outcomes of WD patients presenting to a tertiary care center over a period of 10 years. MATERIAL AND METHODS This retrospective analysis was conducted at Shifa International Hospital, Islamabad, Pakistan. Patients
- Subjects :
- Male
Pediatrics
medicine.medical_specialty
Oral treatment
Adolescent
medicine.medical_treatment
Urinary system
Consanguinity
Disease
Liver transplantation
Hepatolenticular Degeneration
medicine
Humans
Pakistan
Chelation therapy
Child
Retrospective Studies
Transplantation
Original Paper
business.industry
Incidence (epidemiology)
Acute-On-Chronic Liver Failure
Retrospective cohort study
General Medicine
Hospitals, Pediatric
Chelation Therapy
Liver Transplantation
((2,3,7,8,12,13,17,18)-octaethylporphinato)copper (II)
Child, Preschool
Female
business
Subjects
Details
- Language :
- English
- ISSN :
- 23290358 and 14259524
- Volume :
- 26
- Database :
- OpenAIRE
- Journal :
- Annals of Transplantation
- Accession number :
- edsair.doi.dedup.....2fcc18956621c950edbe51beb134f479