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Successful management of anesthesia complications in a child with Crouzon syndrome
- Source :
- Der Anaesthesist. 69:432-435
- Publication Year :
- 2020
- Publisher :
- Springer Science and Business Media LLC, 2020.
-
Abstract
- Crouzon syndrome (CS) is a rare autosomal dominant inherited disorder caused by mutations in the fibroblast growth factor receptor 2 (FGFR2) gene. The disease is characterized by premature fusion of the coronal and sagittal sutures of the skull, resulting in clinical manifestations of midfacial hypoplasia, shallow orbit, maxillary dysplasia, and occasional upper respiratory obstruction. This article presents the case of a child aged 2 years and 7 months with CS scheduled for bilateral tonsillectomy and adenoidectomy. The patient had a difficult procedure of extubation and was reintubated and the tracheal intubation was removed 2 days after surgery. The CS is a rare condition with physical characteristics that can result in difficult airway manipulation. It is important for anesthesiologists to recognize and avoid potential airway complications in the management of such patients through detailed preoperative evaluation and careful observation after surgery to reduce perioperative risks.
- Subjects :
- Male
medicine.medical_specialty
medicine.medical_treatment
Perioperative Care
Adenoidectomy
03 medical and health sciences
0302 clinical medicine
030202 anesthesiology
medicine
Humans
Anesthesia
Tonsillectomy
business.industry
Craniofacial Dysostosis
Anesthesia complication
Tracheal intubation
Crouzon syndrome
030208 emergency & critical care medicine
General Medicine
Perioperative
medicine.disease
Hypoplasia
Surgery
Airway Obstruction
Anesthesiology and Pain Medicine
Child, Preschool
Airway Extubation
Airway
business
Subjects
Details
- ISSN :
- 1432055X and 00032417
- Volume :
- 69
- Database :
- OpenAIRE
- Journal :
- Der Anaesthesist
- Accession number :
- edsair.doi.dedup.....4f686f21c8b8cf01ca3a5a1539ff6af6