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Left Coronary Artery Stenosis Causing Left Ventricular Dysfunction In Two Children With Supravalvular Aortic Stenosis
Left Coronary Artery Stenosis Causing Left Ventricular Dysfunction In Two Children With Supravalvular Aortic Stenosis
- Source :
- World Journal for Pediatric and Congenital Heart Surgery. 6:311-316
- Publication Year :
- 2015
- Publisher :
- SAGE Publications, 2015.
-
Abstract
- Congenital supravalvar aortic stenosis (SVAS) is an arteriopathy associated with Williams-Beuren syndrome (WBS) and other isolated elastin gene deletions. Cardiovascular manifestations associated with WBS are characterized by obstructive arterial lesions such as SVAS and pulmonary artery stenosis in addition to bicuspid aortic valve and mitral valve prolapse. However, coronary artery ostial stenosis may be associated with SVAS, and it increases the risk of sudden death and may complicate surgical management. In this report, we present our experience with two patients having SVAS and left coronary artery ostial stenosis with associated left ventricular dysfunction.
- Subjects :
- Male
Williams Syndrome
congenital, hereditary, and neonatal diseases and abnormalities
medicine.medical_specialty
Heart Valve Diseases
Left Main Coronary Artery Stenosis
Pulmonary Artery
Sudden death
Ventricular Dysfunction, Left
Bicuspid aortic valve
Left coronary artery
Bicuspid Aortic Valve Disease
Internal medicine
medicine.artery
medicine
Humans
Mitral valve prolapse
cardiovascular diseases
Pulmonary artery stenosis
business.industry
Coronary Stenosis
Infant
General Medicine
medicine.disease
Aortic Stenosis, Supravalvular
Pulmonary Valve Stenosis
Stenosis
Aortic Valve
Child, Preschool
Pediatrics, Perinatology and Child Health
cardiovascular system
Cardiology
Female
Surgery
Cardiology and Cardiovascular Medicine
business
Supravalvular aortic stenosis
Subjects
Details
- ISSN :
- 2150136X and 21501351
- Volume :
- 6
- Database :
- OpenAIRE
- Journal :
- World Journal for Pediatric and Congenital Heart Surgery
- Accession number :
- edsair.doi.dedup.....4f708dc92b30b984c515d53d9dba5bd1
- Full Text :
- https://doi.org/10.1177/2150135114563767