Lumbosacral pain: chordoma--a diagnosis not to forget

Chordomas are rare tumours (1-4%) whose origin is remnants of the embryonic primitive foetal notochord. Estimated incidence is 0.51 cases per million. They develop at the neuroaxis ends and on vertebral bodies. Clinical manifestations can differ according to different localizations and to insidious and slow evolution. Our case is an illustration of diagnosis and treatment difficulties. Chordomas remain a diagnosis to be reminded.