Solitary peribiliary cyst mimicking cholangiocarcinoma

Summary Peribiliary cysts are cystic dilatations of the peribiliary glands, which are normal structures of the bile ducts. There are most often multiple lesions in patients presenting with obstructive jaundice. Most patients have underlying liver diseases. In our patient, obstructive jaundice was first noted. There were no associated liver diseases. Imaging studies showed a solitary hypodense lesion in the hilar area, and the first impression was of a Klatskin tumor. During the operation, a peribiliary cyst was noted and, after fenestration of the cyst, the obstructive jaundice subsided. There are, to the best of our knowledge, only two cases such as ours in the English-language literature.