Double inlet left ventricle with unrestricted pulmonary blood flow and survival into adulthood

A 21-year-old male refugee from Syria with known but ill-defined congenital heart disease, presented with palpitations, no signs of heart failure, and near normal oxygen saturation. Chest radiography showed a globally enlarged heart with prominent hilar and pulmonary vessels ( Panel A ). Transthoracic echocardiography revealed a double-inlet-left-ventricle (DILV) with good systolic function ( Panel B ), malposition of the …