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Low-grade adenocarcinoma of endolymphatic sac origin
Low-grade adenocarcinoma of endolymphatic sac origin
- Source :
- American journal of otolaryngology. 27(5)
- Publication Year :
- 2005
-
Abstract
- We present a case of papillary cystic low-grade adenocarcinoma of endolymphatic sac origin. These tumors are very rare and only a few cases have been reported in literature. They have a protracted clinical course causing progressive invasion and bony destruction. Radiologically, they appear as a heterogenous lobulated vascular mass, invading bone and compressing surrounding structures. Histologically, these tumors are composed of uniform population of cells, resembling normal endolymphatic sac epithelium. This causes considerable diagnostic difficulty. A strong index of suspicion along with clinical and radiological correlation is essential to arrive at a correct diagnosis. In some bilateral cases, association with von Hippel–Lindau disease has been noted. Radical mastoidectomy and temporal bone resection, which may sometimes necessitate sacrifice of cranial nerves, is the treatment of choice.
- Subjects :
- Adult
Male
Pathology
medicine.medical_specialty
Population
Adenocarcinoma
Endolymphatic sac
Tinnitus
Temporal bone
medicine
Humans
education
Ear Neoplasms
education.field_of_study
business.industry
Cranial nerves
Clinical course
Headache
medicine.disease
Immunohistochemistry
Magnetic Resonance Imaging
medicine.anatomical_structure
Otorhinolaryngology
Radical mastoidectomy
Disease Progression
Neurosurgery
Endolymphatic Sac
business
Tomography, X-Ray Computed
Subjects
Details
- ISSN :
- 01960709
- Volume :
- 27
- Issue :
- 5
- Database :
- OpenAIRE
- Journal :
- American journal of otolaryngology
- Accession number :
- edsair.doi.dedup.....c51c85a8a7b52c6d931018653b8395f1