Back to Search
Start Over
Pulmonary veno-occlusive disease in a patient with recently diagnosed systemic sclerosis
- Source :
- van Leeuwen, N M, Ramiro, S, Ninaber, M K, Nossent, E & de Vries-Bouwstra, J K 2020, ' Pulmonary veno-occlusive disease in a patient with recently diagnosed systemic sclerosis ', Journal of Scleroderma and Related Disorders, vol. 5, no. 2, pp. NP1-NP4 . https://doi.org/10.1177/2397198319852194, Journal of Scleroderma and Related Disorders, 5(2), NP1-NP4. SAGE Publications Ltd, Journal of Scleroderma and Related Disorders, 5(2), NP1-NP4. SAGE PUBLICATIONS LTD
- Publication Year :
- 2020
-
Abstract
- Pulmonary veno-occlusive disease is a rare cause of pulmonary hypertension in patients with systemic sclerosis that can be misclassified as pulmonary arterial hypertension. Differentiation between pulmonary veno-occlusive disease and pulmonary arterial hypertension is challenging because of the similar clinical picture. Nevertheless, discrimination is important because pulmonary veno-occlusive disease has a worse prognosis. Vasodilators including phosphodiesterase type 5 inhibitors and endothelin receptor antagonists should be started with caution and often in combination with diuretics to prevent pulmonary edema.
- Subjects :
- medicine.medical_specialty
business.industry
Immunology
Disease
medicine.disease
Connective tissue disease
Pulmonary hypertension
Scleroderma
surgical procedures, operative
Rheumatology
connective tissue disease
Internal medicine
pulmonary arterial hypertension
medicine
Cardiology
Immunology and Allergy
Systemic sclerosis
In patient
scleroderma
Pulmonary Veno-Occlusive Disease
cardiovascular diseases
business
pulmonary veno-occlusive disease
Subjects
Details
- Language :
- English
- ISSN :
- 23971983
- Database :
- OpenAIRE
- Journal :
- van Leeuwen, N M, Ramiro, S, Ninaber, M K, Nossent, E & de Vries-Bouwstra, J K 2020, ' Pulmonary veno-occlusive disease in a patient with recently diagnosed systemic sclerosis ', Journal of Scleroderma and Related Disorders, vol. 5, no. 2, pp. NP1-NP4 . https://doi.org/10.1177/2397198319852194, Journal of Scleroderma and Related Disorders, 5(2), NP1-NP4. SAGE Publications Ltd, Journal of Scleroderma and Related Disorders, 5(2), NP1-NP4. SAGE PUBLICATIONS LTD
- Accession number :
- edsair.doi.dedup.....ce813d70c27b902d32a7672f2bbc1659