Intraventricular liponeurocytoma: The role of surgery and adjuvant therapy

Background: After a series of case reports, in the WHO classification of 2007, liponeurocytomas were reclassified as grade II tumors and confirmed in the last WHO classification of 2016. We describe a rare case of intraventricular location of liponeurocytoma with review of the literature and propose the management of these rare lesions. Methods: We reviewed the pertinent english literature and extracted 9 articles to discuss 12 cases of intraventricular liponeurocytoma. We reported demographics and clinical data cases including our case. Results: Patients mean age is 37years. There is a male prevalence. All 12 patients underwent surgical treatment. A total tumor resection was obtained in 66,6%. There is one mortality reported due to intraventricular hemorrhage. In 4 cases K67/MIB-1 resulted 3% after subtotal removal. Keywords: Liponeurocytoma, Fourth ventricle, Ki-67 index, Neurocytoma