Hepatic Abscess due to Burkholderia (Pseudomonas) cepacia in Cystic Fibrosis

Burkholderia (Pseudomonas) cepacia has been cultured from bronchial secretions of patients with cystic fibrosis with varying frequency. The overall prevalence in patients over 18 years old at the authors’ centre in Toronto is 51%. Extrapulmonary infections are rare in nonimmunosuppressed patients with cystic fibrosis and B cepacia has been the causative organism in only three previous reports. Two patients with cystic fibrosis are described who developed hepatic abscesses clue to B cepacia. One patient is the sibling of two brothers in whom this complication was previously described.