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Dermatomyositis, clinically presenting with cutaneous ulcers, with histopathologic evidence of perforating collagenosis

Authors :
Rachel, Rosenstein
Kathryn, Martires
Mitalee, Christman
Vitaly, Terushkin
Shane A, Meehan
Nicole, Seminara
Brian D, Golden
Andrew G, Franks
Source :
Dermatology online journal. 22(12)
Publication Year :
2016

Abstract

Dermatomyositis is a systemic, autoimmune diseasewith a variety of clinical features that often includemyositis and characteristic cutaneous findings. Asubset of patients with dermatomyositis developcutaneous ulcers, often in the setting of vasculitis orvasculopathy. We present a case of dermatomyositiswith cutaneous ulcers that show perforatingcollagenosis on histopathologic examination.Acquired reactive perforating collagenosistypically occurs in the setting of diabetes mellitus,chronic renal failure, and other pruritic conditions,and this case represents a rare association withdermatomyositis, which may ultimately be helpful inelucidating the pathophysiology of this perforatingdisorder.

Details

ISSN :
10872108
Volume :
22
Issue :
12
Database :
OpenAIRE
Journal :
Dermatology online journal
Accession number :
edsair.pmid..........e8b6bf4ff06d0f5429bad38ca5a9cc40