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Isolated nonpulsatile enophthalmos in neurofibromatosis: An uncommon entity
- Source :
- Indian Journal of Ophthalmology, Vol 65, Iss 10, Pp 1063-1066 (2017)
- Publication Year :
- 2017
- Publisher :
- Wolters Kluwer Medknow Publications, 2017.
-
Abstract
- Isolated enophthalmos is a rarely observed entity in neurofibromatosis (NF). A 12-year-old male presented with right lower eyelid fat prolapse and enophthalmos for the past 7 years. There was no history of antecedent trauma/surgery. Computed tomography of orbit revealed an ill-defined intraconal hyperdense lesion located between lateral and inferior rectus along with an enlarged inferior orbital fissure (IOF). Superior orbital fissure was minimally widened without prolapse of any intracranial contents. Excision biopsy along with repair of widened IOF was performed through inferior transconjunctival route. Histopathology was suggestive of plexiform neurofibroma with positivity for S-100 and epithelial membrane antigen. No associated cutaneous lesions were present. Nonpulsatile enophthalmos with eyelid fat prolapse can be a presenting sign of NF.
- Subjects :
- Bony orbit
enophthalmos
neurofibromatosis
Ophthalmology
RE1-994
Subjects
Details
- Language :
- English
- ISSN :
- 03014738 and 19983689
- Volume :
- 65
- Issue :
- 10
- Database :
- Directory of Open Access Journals
- Journal :
- Indian Journal of Ophthalmology
- Publication Type :
- Academic Journal
- Accession number :
- edsdoj.0f1b370db90a4c2582c65f6a58fa26ba
- Document Type :
- article
- Full Text :
- https://doi.org/10.4103/ijo.IJO_396_17