Nonspecific aortoarteritis with lesion of the left branch of the pulmonary artery (Takayasu's disease)

The goal is to describe a clinical case of a patient with nonspecific aortoarteritis. A special feature of this case is the lesion of the left branch of the pulmonary artery, the progression of the disease with the development of pulmonary hypertension and dilatation of the right heart, combined defeat of the descending thoracic aorta and brachiocephalic arteries. The issues of long-term course of the disease and the difficulties of diagnosis are discussed, in order to help practitioners of different profiles to increase the detectability and early diagnosis of this disease.