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Orbital cellulitis and massive chemosis as first sign of a cilio-choroidal malignant melanoma without extraocular extension: A case report
- Source :
- Current Problems in Cancer: Case Reports, Vol 11, Iss , Pp 100253- (2023)
- Publication Year :
- 2023
- Publisher :
- Elsevier, 2023.
-
Abstract
- Purpose: To describe a case of cilio-choroidal melanoma presenting as aseptic orbital cellulitis with massive conjunctival chemosis. Methods: Case report. Results: A 51-year-old man with a left retro-iris pigmented lesion had acute lid edema, conjunctival chemosis, and extensive hyphema. Ultrasound revealed a large, lobulated, wide-base choroidal-starting lesion affecting the ciliary bodies and vitreous chamber. MRI revealed low-intermediate T2-signal and intermediate-high T1-signal, with substantial post-contrastographic enhancement. After one week of systemic corticosteroids, the chemosis reduced significantly, and the patient was referred for enucleation, even without histologic confirmation. Post-surgical histopathology found 90% necrotic tissue, few viable cells, and no scleral or vascular invasion, with genetic analysis showing monosomy of chromosome 3 and 8q gain. Conclusion: Choroidal melanoma, particularly if necrotic, may occasionally present as aseptic orbital cellulitis, even without extraocular spread.
Details
- Language :
- English
- ISSN :
- 26666219
- Volume :
- 11
- Issue :
- 100253-
- Database :
- Directory of Open Access Journals
- Journal :
- Current Problems in Cancer: Case Reports
- Publication Type :
- Academic Journal
- Accession number :
- edsdoj.44bd8f4124f541e7a95615ab05da0ba0
- Document Type :
- article
- Full Text :
- https://doi.org/10.1016/j.cpccr.2023.100253