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Treatment of skeletal and non-skeletal alterations of Mucopolysaccharidosis type IVA by AAV-mediated gene therapy

Authors :
Joan Bertolin
Víctor Sánchez
Albert Ribera
Maria Luisa Jaén
Miquel Garcia
Anna Pujol
Xavier Sánchez
Sergio Muñoz
Sara Marcó
Jennifer Pérez
Gemma Elias
Xavier León
Carles Roca
Veronica Jimenez
Pedro Otaegui
Francisca Mulero
Marc Navarro
Jesús Ruberte
Fatima Bosch
Source :
Nature Communications, Vol 12, Iss 1, Pp 1-14 (2021)
Publication Year :
2021
Publisher :
Nature Portfolio, 2021.

Abstract

Mucopolysaccharidosis type IVA (MPSIVA) is a lysosomal storage disorder causing severe skeletal and non-skeletal alterations in patients. Here, the authors generate a MPSIVA rat model that mimics the disabling human pathology and develop an AAV9-Galns gene therapy to treat the disease.

Subjects

Subjects :
Science

Details

Language :
English
ISSN :
20411723
Volume :
12
Issue :
1
Database :
Directory of Open Access Journals
Journal :
Nature Communications
Publication Type :
Academic Journal
Accession number :
edsdoj.4ba8f5aa92cf4b558796ff21512a7699
Document Type :
article
Full Text :
https://doi.org/10.1038/s41467-021-25697-y