Complex reconstruction/ replacement of both hip and knee joints in advance stage of ochronotic arthropathy- A case report

Background: Ochronotic Arthropathy is very rare disorder (around one in million people). It is due to deficiency of enzyme homogentisic acid oxidase which leads to accumulation of homogentisic acid (HGA) and causes damage of several connective tissues. Case report: 53 years old male presented with pain and stiffness in both hip and knee since last 10 years, knees were more painful than hips. In last 6 months his condition deteriorated which hampered his daily routine activities. There is history of consanguineous marriage in family, his two sons also suffering from same problems. Intra-operative we found blackish discolouration of soft tissue and cartilage. Conclusion: Fabulous results have been seen after bilateral hip and knee replacement at 18 months of follow up without any complications.