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Loss of the Arp2/3 complex component ARPC1B causes platelet abnormalities and predisposes to inflammatory disease

Authors :
Walter H. A. Kahr
Fred G. Pluthero
Abdul Elkadri
Neil Warner
Marko Drobac
Chang Hua Chen
Richard W. Lo
Ling Li
Ren Li
Qi Li
Cornelia Thoeni
Jie Pan
Gabriella Leung
Irene Lara-Corrales
Ryan Murchie
Ernest Cutz
Ronald M. Laxer
Julia Upton
Chaim M. Roifman
Rae S. M. Yeung
John H Brumell
Aleixo M Muise
Source :
Nature Communications, Vol 8, Iss 1, Pp 1-14 (2017)
Publication Year :
2017
Publisher :
Nature Portfolio, 2017.

Abstract

ARPC1B is a component of the actin-related protein 2/3 complex (Arp2/3), which is required for actin filament branching. Kahret al. show that ARPC1B deficiency in humans is associated with severe multisystem disease that includes platelet abnormalities, eosinophilia, eczema and other indicators of immune disease.

Subjects

Subjects :
Science

Details

Language :
English
ISSN :
20411723
Volume :
8
Issue :
1
Database :
Directory of Open Access Journals
Journal :
Nature Communications
Publication Type :
Academic Journal
Accession number :
edsdoj.6b90418cc417ea55ca5834ef97650
Document Type :
article
Full Text :
https://doi.org/10.1038/ncomms14816