A Rare Case of Huge Renal Leiomyosarcoma and Imaging Diagnostic Dilemma

Soft tissue sarcomas are rare mesenchymal tumours. Leiomyosarcoma is a rare malignant tumour of smooth muscle origin that generally arises from soft tissues and uterine tissue. On occasions, they may arise from smooth muscle of the vessel walls, more commonly from the veins. Renal leiomyosarcomas frequently originates from the smooth muscles of renal capsule, renal pelvis or renal vessels. Correct diagnosis and appropriate management is very essential in such cases. We highlight the possibility of malignant soft tissue sarcoma like leiomyosarcoma in the kidney. We emphasize on the suspicion of rare possibility and clinicopathological correlation is required to identify such cases, which has pronounced prognostic implications as whether to do surgical resection or biopsy or treat such patient with chemotherapy or radiotherapy vary with diagnosis.