Extraventricular neurocytoma located within the splenium of the corpus callosum

Central neurocytomas (CNs) are rare intraventricular tumors that are well demarcated and display neuronal differentiation. This tumor type is most frequently diagnosed in young adults and is typically located at the septum pellucidum and fornix, and presents with intracranial hypertension due to obstructive hydrocephalus. Extraventricular neurocytomas (EVNs) are rare neuronal tumors with biological and histopathological characteristics similar to CNs, but which arise from the extraventricular parenchymal tissue (Giangaspero et al., 1997) Giangaspero et al. (1997) [4]. Extraventricular neurocytomas are included in the definition of neoplasms in the 2007 World Health Organization classification of tumors of the central nervous system [6]. These atypical locations are mostly in the cerebral hemispheres that are commonly identified in the frontal and parietal lobes. However, there have been some reports of EVNs located in the thalamus, cerebellum, pineal region, and even in the spinal cord (McCutchen et al., 1999; Stephan et al., 1999; Tortori-Donati et al. 1999) McCutchen et al. (1999), Stephan et al. (1999), Tortori-Donati et al. (1999) [7,13,14]. In this manuscript, we report an extremely rare case of an EVN arising from the splenium of the corpus callosum, and review the relevant literature and management of such lesions.