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Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome

Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome

Authors :
Emmanuel I. González-Moreno
Carlos R. Cámara-Lemarroy
David O. Borjas-Almaguer
Sylvia A. Martínez-Cabriales
Jonathan Paz-Delgadillo
Rodrigo Gutiérrez-Udave
Ana S. Ayala-Cortés
Jorge Ocampo-Candiani
Carlos A. Cortéz-Hernández
Héctor J. Maldonado-Garza
Source :
Annals of Hepatology, Vol 14, Iss 3, Pp 416-419 (2015)
Publication Year :
2015
Publisher :
Elsevier, 2015.

Abstract

Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.

Details

Language :
English
ISSN :
16652681
Volume :
14
Issue :
3
Database :
Directory of Open Access Journals
Journal :
Annals of Hepatology
Publication Type :
Academic Journal
Accession number :
edsdoj.b12132291a3c486a97f08aae8390bf45
Document Type :
article
Full Text :
https://doi.org/10.1016/S1665-2681(19)31283-9