Back to Search Start Over

Giant omphalocele with right lung agenesia and bronchial tracheal hypoplasia: A case report

Authors :
Giuseppe De Bernardo
Marta Giovengo
Desiree Sordino
Maurizio Giordano
Massimo Zeccolini
Source :
Radiology Case Reports, Vol 19, Iss 11, Pp 5535-5538 (2024)
Publication Year :
2024
Publisher :
Elsevier, 2024.

Abstract

The omphalocele is an abdominal wall defect at the base of the umbilical cord, with the worldwide prevalence of 2.6 per 10,000 births. Omphalocele contains herniated abdominal organs and is classified in small and giant based on the size of the defect. Omphalocele is associated with several syndromes or structural anomalies. We reported a case of giant omphalocele of 6 cm with right lung agenesis with tracheal and right bronchial hypoplasia. Laryngeal mask stabilized the newborn allowing endotracheal intubation. Due to serious malformations, the newborn died after few hours of life for cardio-respiratory arrest. Early and accurate prenatal diagnosis allows a better intervention strategies in delivery room, improving the chances of survival and reducing complications for infants with omphalocele.

Details

Language :
English
ISSN :
19300433
Volume :
19
Issue :
11
Database :
Directory of Open Access Journals
Journal :
Radiology Case Reports
Publication Type :
Academic Journal
Accession number :
edsdoj.f13aa258cc534503bcd98e241f7f70a5
Document Type :
article
Full Text :
https://doi.org/10.1016/j.radcr.2024.08.069